Congenital Amniotic Bands: Our Experience of 10 Cases.

Abstract

Congenital Constriction bands syndrome or congenital amniotic band syndrome affects 1 in 15,000 births 1. In its severest form it presents as intrauterine amputations but moderate form constriction rings on the extremities at birth. We treated 10 cases in a period of 3 ½ year form May 1993 to Oct 1996. The age of patients at presentation ranged from less than one day to 3 months. In 3 patients (30%) operative treatment was carried out within 24 hours of presentation. 3 (30%) underwent surgical treatment with one week of presentation. 2 patients (20%) had operative treatment in 9 months -1 year. Two patients did not have any surgical treatment. Early treatment was carried out because of progressive swelling or discoloration of the extremity. The treatment comprised of excision of the ring and multiple Z plastics. There was immediate improvement in the colour and swelling of distal part.