Sturge-Weber-Dimitri Syndrome - An integral part of Phakomatosis. A study evaluation of 7 cases in the Department of Radiology, Mayo Hospital, Lahore

Abstract

Sturge Weber Syndrome, is a comparatively rare syndrome .The patient can present with facial manifestations, CNS manifestations, orbital anomalies and visceral manifestations. In the last one year we encountered seven cases which were classical as far as the imaging of these lesions is concerned. These lesions were evaluated on plain film radiography and the state of art Computed Tomography, in one case the dynamic CT scan of the brain was also done. In this article we present the imaging of these seven cases.